DIFFUSE ARTER IAL ECTASIA IN MARFAN SYNDROME
Authors
Abstract:
A 22 year old male referred with palpitation. General appearance and physical exam impressed us in that the patient has Marfan syndrome. Cardiac catheterization showed diffuse arterial ectasia. We found no previous report of this generalized diffuse ectasia.
similar resources
diffuse arter ial ectasia in marfan syndrome
a 22 year old male referred with palpitation. general appearance and physical exam impressed us in that the patient has marfan syndrome. cardiac catheterization showed diffuse arterial ectasia. we found no previous report of this generalized diffuse ectasia.
full textMeasurement of Reti Nal Arter Ial P '
T IIE importance of the retinal blood vessels in physical diagnosis has always been emphasized. However, it is only in recent years that physicians have appreciated a simnple technic for measuring the pressure within these vessels. "Ophthalmodyniamioimietry ' is the determination of retinal artery pressure by application of a measured external force to the selera, combined with ophthalmoscopie ...
full textDural ectasia in Marfan syndrome: a case control study.
BACKGROUND AND PURPOSE Dural ectasia (DE) is one of the major criteria of Marfan syndrome (MFS). Our aim was to establish the prevalence of DE in an adult population fulfilling the Ghent criteria for MFS and to assess definitions of DE. MATERIALS AND METHODS One hundred five adults with suspected MFS were included. MR imaging at 1.5T was performed unless contraindicated; then CT was obtained....
full textDural ectasia as presenting symptom of Marfan syndrome.
• Vol 10 • March 2008 194 Marfan syndrome is a genetic, dominant, systemic connective tissue disease with variable clinical features, some of which are life threatening. The prevalence is 1:10,000 live births [1]. The syndrome results from mutations in the FBN1 gene, on chromosome 15, which encodes for the fibrillin 1 protein. Fibrillin is an important compound in the extracellular matrix and t...
full textDIFFUSE CORONARY ARTERIAL ECTASIA WITH HYPERTROPHIC CARDIOMYOPATHY
A 40 year old male, a known case of hypertrophic cardiomyopathy, was admitted for catheterization. At catheterization and angiography, septum was hypertrophied to about 5cm and diffuse coronary artery aneurysm was revealed. We found no previous report of coronary artery aneurysm in hypertrophic cardiomyopathy.
full textPrevalence of Dural Ectasia in Loeys-Dietz Syndrome: Comparison with Marfan Syndrome and Normal Controls
BACKGROUND AND PURPOSE Dural ectasia is well recognized in Marfan syndrome (MFS) as one of the major diagnostic criteria, but the exact prevalence of dural ectasia is still unknown in Loeys-Dietz syndrome (LDS), which is a recently discovered connective tissue disease. In this study, we evaluated the prevalence of dural ectasia in LDS according by using qualitative and quantitative methods and ...
full textMy Resources
Journal title
volume 8 issue 1
pages 63- 64
publication date 1994-05
By following a journal you will be notified via email when a new issue of this journal is published.
Hosted on Doprax cloud platform doprax.com
copyright © 2015-2023